Gliomatosis cerebri mimicking Rasmussen encephalitis: Case report

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    Abstract

    Gliomatosis cerebri (GC) is a distinct malignant neuroepithelial neoplasm that is rarely found in children. The authors present the case of an 11-year-old girl in whom the initial presentation suggested possible early Rasmussen encephalitis (RE), but in whom a diagnosis of GC was made instead after examination of a brain biopsy specimen. Despite advances in magnetic resonance (MR) imaging and MR spectroscopy, this case shows the limitations of clinical and neuroimaging diagnosis and the essential role of biopsy procedures when early RE is suspected.

    Original languageEnglish
    Pages (from-to)143-146
    Number of pages4
    JournalJournal of neurosurgery
    Volume107
    Issue number2 SUPPL.
    DOIs
    StatePublished - Aug 2007

    ASJC Scopus Subject Areas

    • Surgery
    • Clinical Neurology

    Keywords

    • Biopsy
    • Gliomatosis cerebri
    • Magnetic resonance spectroscopy
    • Pediatric neurosurgery
    • Rasmussen encephalitis
    • Diagnosis, Differential
    • Magnetic Resonance Spectroscopy
    • Humans
    • Encephalitis/diagnosis
    • Magnetic Resonance Imaging
    • Female
    • Brain Neoplasms/diagnosis
    • Child
    • Neoplasms, Neuroepithelial/diagnosis

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